Repetitive behaviour profiles in Williams syndrome: Cross syndrome comparisons with Prader-Willi and Down syndromes

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Author(s)
Royston, R
Oliver, C
Moss, J
Adams, D
Berg, K
Burbidge, C
Howlin, P
Nelson, L
Stinton, C
Waite, J
Griffith University Author(s)
Year published
2018
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Show full item recordAbstract
This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader–Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader–Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated ...
View more >This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader–Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader–Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.
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View more >This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader–Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader–Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.
View less >
Journal Title
Journal of Autism and Developmental Disorders
Copyright Statement
© 2017 Springer Netherlands. This is an electronic version of an article published in Journal of Autism and Developmental Disorders, Volume 48, Issue 1, pp 326–331. Journal of Autism and Developmental Disorders is available online at: http://link.springer.com/ with the open URL of your article.
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This publication has been entered into Griffith Research Online as an Advanced Online Version.
Subject
Special education and disability
Psychology
Other psychology not elsewhere classified