The Cardiac Society of Australia and New Zealand Position Statement on the Diagnosis and Management of Arrhythmogenic Right Ventricular Cardiomyopathy (2019 Update)

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Embargoed until: 2021-04-23
Author(s)
Hamilton-Craig, Christian
McGavigan, Andrew
Semsarian, Chris
Martin, Andrew
Atherton, John
Stanton, Tony
La Gerche, Andre
Taylor, Andrew J
Haqqani, Haris
Year published
2020
Metadata
Show full item recordAbstract
Key Points:
1. Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a disease affecting the right, and/or the left ventricle, and commonly presents as an electrical disorder with ventricular arrhythmias and increased risk of sudden cardiac death.
2. ARVC cannot be diagnosed by a single test, and is a clinical diagnosis supported by electrophysiologic, morpho-functional, genetic, and histological data based on the 2010 Task Force 2 criteria.
3. Familial involvement occurs in more than 50%, and referral to a specialist centre with access to genotyping is appropriate in selected cases.
4. Implantable cardioverter-defibrillator ...
View more >Key Points: 1. Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a disease affecting the right, and/or the left ventricle, and commonly presents as an electrical disorder with ventricular arrhythmias and increased risk of sudden cardiac death. 2. ARVC cannot be diagnosed by a single test, and is a clinical diagnosis supported by electrophysiologic, morpho-functional, genetic, and histological data based on the 2010 Task Force 2 criteria. 3. Familial involvement occurs in more than 50%, and referral to a specialist centre with access to genotyping is appropriate in selected cases. 4. Implantable cardioverter-defibrillator (ICD) therapy carries risk, and appropriate thresholds should apply before offering this, particularly in younger individuals.
View less >
View more >Key Points: 1. Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a disease affecting the right, and/or the left ventricle, and commonly presents as an electrical disorder with ventricular arrhythmias and increased risk of sudden cardiac death. 2. ARVC cannot be diagnosed by a single test, and is a clinical diagnosis supported by electrophysiologic, morpho-functional, genetic, and histological data based on the 2010 Task Force 2 criteria. 3. Familial involvement occurs in more than 50%, and referral to a specialist centre with access to genotyping is appropriate in selected cases. 4. Implantable cardioverter-defibrillator (ICD) therapy carries risk, and appropriate thresholds should apply before offering this, particularly in younger individuals.
View less >
Journal Title
Heart, Lung and Circulation
Copyright Statement
© 2019 Australasian Society of Cardiac and Thoracic Surgeons and The Cardiac Society of Australia and New Zealand. Published by Elsevier Ltd. Licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International Licence, which permits unrestricted, non-commercial use, distribution and reproduction in any medium, providing that the work is properly cited.
Note
This publication has been entered into Griffith Research Online as an Advanced Online Version.
Subject
Cardiorespiratory Medicine and Haematology
Public Health and Health Services
Arrhythmia
Arrythmogenic right ventricular cardiomyopathy
Genetics
Sudden cardiac death